Oncohema Key

676 Pediatric Oncology Sara E. Helmig and Alberto Pappo Pediatric sarcomas are a heterogeneous group of diseases that can arise in bone or soft tissue and account for approximately 12%…

22116 Tenosynovial Giant Cell Tumor/Pigmented Villonodular Synovitis Edward Y. Cheng, Christian M. Ogilvie, and Paari Murugan The term “pigmented villonodular synovitis” (PVNS) was coined in 1941 and is based upon…

27721 Malignant Peripheral Nerve Sheath Tumor Jack F. Shern and Brigitte C. Widemann Malignant peripheral nerve sheath tumors (MPNSTs) are soft tissue sarcomas that arise from peripheral nerve sheaths. MPNSTs…

25119 Desmoid Tumor Chelsea R. Horwood and Valerie P. Grignol Desmoid tumors, or aggressive fibromatosis, are locally aggressive soft tissue tumors that do not have the ability to metastasize. The…

31524 Chordoma Jomjit Chantharasamee, Francis Hornicek, and Arun S. Singh Chordomas are rare bone tumors accounting for ~4% of all bony malignancies. Clinically, these tumors typically grow slowly, but act…

29923 Endometrial Stromal Sarcoma Stéphanie Gaillard and Angeles Alvarez Secord Endometrial stromal sarcoma (ESS) represents a very rare subset of uterine mesenchymal neoplasms and endometrial stromal tumors. Endometrial stromal tumors…

535 Surgical Approach and Surgical Reconstruction Options in Treatment of Bone Sarcomas Erika L. Garbrecht, Motasem Al Maaieh, Sheila Ann Conway, and Juan A. Pretell Patients with sarcoma of the…

26520 Undifferentiated Pleomorphic Sarcoma/Myxofibrosarcoma/Other Fibrosarcomas Gabriel Tinoco and David Liebner Undifferentiated pleomorphic sarcoma (UPS) encompasses malignant neoplasms of mesenchymal origin, which demonstrate cellular pleomorphism and which lack evidence of cellular…

19914 Ewing Sarcoma Warren Alperstein and Matteo Trucco The Ewing sarcoma (ES) family of tumors is a group of tumors consisting of typical ES, extraosseous ES, atypical ES, primitive neuroectodermal…